Cells, Cell Division, and Chromosomes

I.    CELL: To understand the structure and function of the genetic information (DNA), you must
      understand cells.  This is where DNA is and where it functions.
A.    Cell Biology
        1.    1665 - Robert Hooke - cork  - 'cells'
        2.    1805 - Lorenz Oken stated: "All organic beings originate from and consist of vesicles or cells."
        3.    1809 - Jean Baptiste de Lamarck: "No body can have life if its constituent parts are not
                         cellular  tissue or are not formed by cellular tissue."
        4.    1838 - Matthais Schleiden (Botanist)
               1839 - Theodor Schwann (Zoologist)
                Credited with the Cell Theory "all animals and plants are composed of cells."
         5.    1858 - Rudolph Virchow: "Omnis cellula e cellula"  All cells come from previously existing
                          cells - no spontaneous generation.
         6.    1862 - Louis Pasteur: no spontaneous generation definitively supported
B.    The Role of Chromosomes
        1.    1868 - Freidrick Miescher: purified an acidic, non-proteinaceous substance high in
                         phosphorus, with no sulfur, from cell nuclei "nuclein".
        2.    1879 - Walther Flemming: used red dye to stain nuclei and found granules he called
                         "chromatin".  By staining cells in process of dividing, he saw "chromatin" coalesce into
                         thread like bodies "chromosomes".  these bodies were separated during the process
                         he called mitosis.
        3.    1900 - Mendel's laws of segregation and independent assortment rediscovered by Correns,
                         Tchermak, and DeVries.
        4.    1902 + 1903 - Walter Sutton and Theodore Boveri: described the movement of chromosomes
                         during gamete formation (meiosis) and explained how this complemented Mendel's
                         Laws.  Suggested that chromosomes carry genetic information.

            The Chromosomal Theory of Inheritance: genetic information must -
                - replicate
                - store information
                - control expression of information (regulate)
                - mutate

So, by 1905, we knew what cells were and the role of chromosomes as vectors of genetic information was implicated.  How do cells work?

II.    Review of Cell Biology
    A.    Structures
        1.    Plasma (Cell) Membrane (animals) : Plasmalemma (plants):
                a.    1972 Sanger & Nicholson "Fluid Mosaic Model"  proteins floating in a phospholipid
                       bilayer.
                b.    Control the transport of molecules into and out of the cell.
                c.    Cell-Cell recognition:
                             Cell Coat:  glycoproteins and polysaccharides antigenic determinants (AB & MN)
                                              histocompatibility antigens
                d.    act as a reactive surface (lots of enzymes)
                e.    Duchenne Muscular Dystrophy:  loss of function of dystrophin which functions at the cell
                       membrane in muscles
        2.    Cell Wall:
                a.    Plants:  cellulose
                b.    Bacteria:  peptidoglycan (protein and sugar)
                        i.    Capsule: mucopolysaccharide
                        ii.   Diplococcus pneumonia: virulence and nonvirulence depending on presence or
                              absence of capsule
        3.    Nucleus: porous bi-membrane sac around the DNA.  In bacteria do not have a nucleus, have a
               nucleoid peripheral region where DNA is concentrated.
                    Chromatin:  DNA + Histones (basic proteins) - uncoiled
                    Chromosomes:  Condensed chromatin (mitosis and meiosis)
                    Nucleolus:  synthesis of rRNA, and ribosome construction
                    NOR:  Nucleolus Organizer Region: area of DNA encoding rRNA
        4.    Cytoplasm:
                a.    Cytosol: nonparticulate, colloidal material called
                b.    Cytoskeleton: complex of tubules and filaments which hold organelles in place.
                        Microtubules:  tubulin
                        Microfilaments:  actin
        5.    Endoplasmic Reticulum: network of membranous vesicles that may be continuous with the
               nucleus.
                        Smooth: fatty acid and phospholipid synthesis
                        Rough: studded with ribosomes, protein synthesis
        6.    Mitochondria : site of aerobic respiration for energy production.
                Oxidative Phosphorylation
                    C6H12O6  =>  6CO2 + 6H2O
        7.    Chloroplast: site of Photophosphorylation
                    6CO2 + 6H2O  => C6H12O6
                Endosymbiont Theory:
                    Both mitochondria and chloroplast contain DNA .  Can duplicate themselves and
                    transcribe and translate their genetic information.  Resemble prokaryotic cells.
                    Once free living structures that established a symbiotic relationship with a primitive
                    eukaryotic cell
        8.    Golgi apparatus: series of pancake-like membranous envelopes formed at the end of the ER
               tubules.  Site of protein modification.
        9.    Ribosomes: Protein and rRNA structures that read mRNA and create polypeptides.
        10.  Centrioles: (animals and some lower plants) contained in a region called the centrosome.
               Associated with spindle fibers in mitosis and meiosis.  Derived from the Basal Body
               which has the characteristic 9 X 2 morphology.  Contain their own DNA for replication.

III.    Homologous Chromosomes, Haploidy, and Diploidy
    A.    Homologous Chromosomes:  Chromosomes that synapse or pair during meiosis.
           Chromosomes that are identical with respect to their genetic loci and cetromere placement.
        1.    Metaphase chromosomes have distinctive shapes and lengths
        2.    Each has a condensed centromere
            Centromere:  Specialized region of a chromosome to which the spindle fibers attach during cell
            division.  Location of the centromere determines the shape of the crhomosome during the
            anaphase portion of cell division.  Also known as the primary construction.
            a.    metacentric:  middle
            b.    submetacentric:  between middle and end
            c.    acrocentric:  close to end
            d.    telocentric:  at end
        3.    Arms of the chromosome
            a.    p arm: petite, short arm, above centromere
            b.    q arm: q comes after p, long arm, below centromere
        4.    Each somatic cell within members of the same species contain an identical number of
               chromosomes:  the Diploid Number
            a.    2n: each chromosome exists in pairs or homologous chromosomes
            b.    Contain identical gene sties:  locus (sing.) loci (pl.)
            c.    Have identical genetic potential
            d.    Sexual Reproduction:  one set obtained from each parent - biparental inheritance
            e.    Thus: each diploid organism contains two copies of each gene.  Alternative forms of the
                   same gene are called alleles
    B.    Sex-determining chromosomes:  the exception to the rule
        1.    May not be homologous is size, centromere placement, arm ratio, or genetic potential
        2.    In most mammals and insects:  the male has two different chromosomes (XY) called
               heterogametic sex and females have homogametic sex (XX).
        3.    When the reverse is true (birds):  Females are designated ZW and males ZZ.
    C.    Karyotype:  display of the chromosomes for an organism
    D.    Sister Chromatids:  each individual strand of a duplicated chromosome
    E.    Haploid Genome:  the total set of genes contained on one member of each homologous pair of
           chromosomes
        1.    Haplodiploid:   organisms where ploidy in the sexes is different
            a.    bees and wasps:  females 2n, males n
        2.    Supernumerary or B chromosomes:  very small chromosomes which vary in number among
               individuals.  Devoid of important genes
        3.    Microchromosomes:  birds: number of very small chromosome.  hard to count.  Thought to
               carry genes and be in a constant number like larger chromosomes
    F.    Specialized Chromosomes
        1.    Polytene Chromosomes:  A chromosome that has undergone several rounds of DNA
               replication without separation of the re;oicated chromosomes, forming a giant, thick
               chromosome with alined chromosomes producing a characteisic banding pattern.
            a.    many replication cycles of paired homologues without strand separation or cytokinesis
            b.    Various insect dipterans larval cells (salivary, midgut, rectal, and malpighian excretory
                    tubules) and in several species of protozoans and plants.
            c.    Chromomeres: a coiled, beadlike region of a chromosome most easily visible during cell
                   division.  The aligned chromomeres of polytene chromosomes are responsible for their
                   distinct tive banding pattern.
                i.    Heterochromatin: the heavily staining. Late replicating regions of chromosomes that are
                      premeaturely condensed in interphase.
                ii.    Euchromatin:  chromatin or chromosomal regions that are lightly staining and are
                       relatively uncoiled during the interphase protion of the cell cycle.  The region of the
                       chromosomes thought to contain most of the structural genes.
            d.    Chromocenter:  An aggregation of centromeres and heterochromatic elements of polytene
                   chromosomes.  An irregular, densely staining mass of heterochromatin in the
                   chromosomes, with six arm-like extensions of euchromatin, in the salivary glands of
                   Drosophila.  In Drosophila the chromocenter in polytene chromosomes is usually derived
                   from the fusion of the telomers of the chromosomes.
            e.    Puffs - visible manifestations of gene activity.  A localized uncoiling and swelling in a
                   polytene chromosome, usually regarded as a sign of active transcription.
        2.    Lampbrush:  meiotic chromosomes characterized by extended lateral loops, which reach
               maximum extensionduring diplotene.  Although most intensively studied in amphibians, these
               structres occur in meiotic cells of organisms rnging from nsects through humans.
            a.    Meiotic chromosomes
            b.    Oocytes in Diplotene stage of prophase I of meiosis:  Active in directing the metabolic
                   activities of the developing cell
            c.    Homologues are synapsed pairs held together by chiasmata, but not condensed
            d.    Chromomere supports a pair of lateral loops of DNA

IV.    Cell Cycle
    A.    Description
        1.    Interphase (period between mitotic divisions)
            a.    G1: Gap I : Start
                -    active metabolic stage (protein synthesis)
                -    chromosomes diffuse in euchromatic regions.  Heterochromatin still condensed - gives
                     granular look to nucleus "chromatin"
                -    Each chromosome has 1 chromatid
                -    Nucleolus Þ area of high rRNA production
                -    At a point late in G1, cells follow one of two paths:  G0 or S.  Time when dicision is made
                     is called G1 Checkpoint.
            b.    S
                -    DNA replication (synthesis)
                -    each chromosome has 2 chromatids
                -    Euchromatin replicated first, then the heterochromatin is unwound and replicated.
            c.    G2: Gap II
                -    Synthesis of structures required for mitosis - in animals this is centriole.
                -    Preparatory stage for mitosis
            d.    G0
                -    some cells, produced by unspecialized cells that continue to divide, become arrested in a
                     productive, non-reproductive stage = Go.  Phloem, xylem, epidermis, nerve, muscle,
                     RBC.
                -    R (restriction) point - time when decision to go through G1 or G0 is decided
                -    Some cells can remain quiescent in Go, but can be stimulated to return to G1, thus
                     reentering the cycle
        2.    Mitosis
                - Organized division of genetic information (Karyokinesis) and cytoplasm (cytokinesis).
        3.    Length of time in each stage:  cells in culture have characteristic stage lengths.  Usually a
               cell will go through the complete cycle in about 20 hours.
            a.    S and G2 stages are fairly consistent among different cell types
                i.    S depends on cell type and conditions
            b.    G1: most variation in length of time
            c.    M: usually the least amount of time
            d.    In vivo, cycles may be hrs, days, years, usually G1 that varies; S+G2 same.
    C.    Regulation
        1.    In almost all cells, if S is initiated then the cycle is completed through division.  Cue seems to
               be cytoplasmic in origin (Put G1 nucleus in S or G2 cell).
        2.    If it is a protein cue, are there genes that code for it?  Cell Division Cycle (CDC) genes.  Lee
               Hartwell isolated 150 mutants with >50 different mutations that interrupt the cell cycle.  The
               assumption is that the normal gene is then important in correctly regulating the cycle.
        3.    Control of the Cell Cycle:
            a.    Cycle is regulated at three main points called CHECKPOINTS
               i.    G1/S checkpoint:  monitors cell size and status of DNA (whether it is damaged).  Time
                     when cells become committed to proceeding through the cycle and the subsequent steps
                     of mitosis.
                ii.   G2/M checkpoint:  cell physiological conditions are monitored before entering Mitosis.
                      DNA repication and repair is monitored.
                iii.   M checkpoint:  Monitoring of spindle fiber system formation and attachment of spindle
                      fibers to kinetechoresof chromosomes.
            b.    Controlled through the interaction of two types of proteins
                i.    cdc kinases:  enzymes that regulate other proteins by adding phosphate groups obtained
                      from ATP.  One of the first (and possibly most important kinase found) comes from the
                      cdc2 gene which forms the gene product called cdc2 kinase.  Cdc2 kinase may be
                      necessary for entry into the S phase of DNA synthesis.
                ii.    Cyclins:  Kinases phosphorylate cyclins.  This phosphorylation (or dephosphorylation)
                       influences cyclin actvity at the cell cycle checkpoints.  Act as switches to turn-on or
                       turn-off  the cell cycle.  Cyclins are produced intermittently and degraded rapidly,
                       resulting in a pulse of regulatory activity at each point in the cell cycle.  "The successive
                       appearance of different cyclins and their interactions with different cellular composnts
                       seem to propel the cell through the cell cycle in an orderly and precisse fashion." (Klug
                       1997)
                iii.    Cdk protein (cyclin-dependent kinase protein):  the coordination of a cdc kinase with a
                       cyclin.
            c.    p53:  tumor supressor gene.  Active at G1/M checkpoint.  Functions during apoptosis
                  (programmed cell death).  A normal p53 gene product will target cells for distruction if their
                  DNA is found to be damaged during the G1/M checkpoint.
            d.    Oncogenes:  Originally discovered in RNA viruses (retroviruses) oncogenes transform
                   normal cells into malignant cell (continue dividing).  In cells, there are similar genes called
                   proto-oncogenes.  Apparently, viruses have spliced these out, mutated them, and
                   increased the reproductive rate of host cell.

V.    Mitosis
    A.    Centrosome:  differentiated cytoplasmic area just outside the nucleus
        1.    In animals and lower plants prophase involves the migration of two pairs of centrioles to
               opposite ends of the cell in the centrosome
        2.    It is thought that each pair of centrioles consists of one mature unit and a smaller, newly
               formed centriole
        3.    forms axis along which chromosomal separation occurs.
        4.    centrioles responsible for organization of cytoplasmic microtubules into a series of spindle
               fibers.
            a.    although plant, fungi, and certain algae lack centrioles, spindle fibers are apparent during
                   mitosis
            b.    if some other organizer exists, it has not been discovered
    B.    Interphase - chromosomes diffuse, but replicated
    C.    Prophase (1/3 of mitosis)
        1.    centrioles migrate to opposite poles involved with formation of spindle apparatus.
            a.    as centrioles migrate, the nuclear envelope begins to break down
            b.    Nucleolus disintegrates within the nucleus
        2.    Reorganization of cytoskeletal actin strands attached to chromosomes and centrioles.
        3.    Chromatin condenses into distinct chromosomes (supercoil)
            a.    The two parts of each chromosome are called chromatids
            b.    sister chromatids:
        4.    Kinetochore: is actually a granule within the centomere that attaches to spindle fibers during
               mitosis.  Two kinetochores form on opposite faces of the centromere, each attaching one or
               the other member of a pair of sister chromatids to the spindle fibers.
    D.    Prometaphase and Metaphase - alignment of chromosomes on metaphase plate by spindle
            fibers
        1.    Prometaphase:  refers to the period of chromosome movement
        2.    Metaphase:  applies strictly to the chromosome configuration following this movement
        3.    Migration is made possible by the binding of one or more spindle fibers to the kinetochore
               contained within the centromere of each chromosome.  There are two major classes of
               spindle microtubules.
            a.    Kinetochore microtubules have one end near the centrosome region and the other anchored
                   in the kinetochore.
            b.    Nonkinetochore microtubules grow from the centrioles of the centrosome, but have their
                   other ends free.  These sometimes interdigitate with one another, providing a framework to
                   the spindle and maintaining the separation of the two poles during chromosome separation.
    E.    Anaphase: shortest stage
        1.    Sister chromatids separate - reeled to opposite poles by spindle fibers
        2.    Daughter chromosomes: the two newly formed chromosomes
        3.    As chromosomes migrate the spindle elongates, extending the distance between the two
               centrosome regions
    F.    Telophase
        1.    Nuclear membrane reforms at poles
        2.    Cytokinesis
            a.    Animals - furrowing
            b.    Plants - vesicles coalesce and form the cell plate that develops into middle lamella of cell
                   wall.  Primary & Secondary cell walls are deposited on this middle lamella.
    G.    Products
                identical to each other and parent cell
    H.    Regulation - cytoplasmic initiation of S starts S-G2-M (invariant length)
            - division protein accumulates in G1
            - state. in DNA poly
            - Build to threshold levels inhibition lengthens G1

Sexual Reproduction of Multicellular Organisms demands creation of haploid cells, that, when joined will reconstitute original blueprint.

VI.    Meiosis - 'Reduction-Division'
    A.    MEIOSIS 1
        1.     Overview
            a.    Homologous chromosomes pair or synapse to form a bivalent
            b.    Bivalent gives rise to a unit called the tetrad which consists of four chromatids.
            c.    Two divisions
                    i.    reductional - Meiosis I (tetrad separates into dyad)
                    ii.    equational - Meiosis II (dyad splits into two monads)
            d.    Chromosomes may exchange information - crossing over
        2.    Interphase I: same as mitosis
        3.    Prophase I
            a.    Leptonema (n)
                    Leptotene stage - chromosome begin to condense
                    Homology Search:  initial pairing of homologues
            b.    Zygonema
                    Zygotene stage: rough pairing of the homologues
                    Synaptonemal Complex is formed: the paired structures are called bivalents.
            c.    Pachynema
                    Pachytene stage: intimate point by point synapsis of homologous chromosomes
                    Shortening and coiling of paired chromosomes occurs - bivalents thicken
                    Can distinguish sister chromatids Bivalent = Tetrad
                    Crossing over occurs
            d.    Diplonema
                    Crossing over occurs at chiasmata
                    Crossing over involves nonsister chromatids
                    Genetic variability
                    Chromatids begin to separate
            e.    Diakinesis - further shortening of chromosomes and separation.  Linkage to the spindle.
                   Nuclear membrane and nucleolus disappear.
                    Terminalization: the chiasmata move toward the ends of the tetrad
    END OF PROPHASE I
        4.    Metaphase I - chromosomes pair up in metaphase plate.
        5.    Anaphase I - homologous pairs (tetrads) separate to form dyads
                Disjunction:   the separation of tetrads into dyads
                Nondisjunction:  error where separation does not occur
                Random segregation of dyads is the basis for Mendelian principle of independent assortment.
        6.    Telophase I - cytokinesis
    B.    MEIOSIS II - Equational Division
        1.    Interkinesis:  no DNA synthesis.  only a haploid complement (n)
        2.    Prophase II: dyad is composed of one pair of sister chromatids attached by a common
               centromere
        3.    Metaphase II:  centromeres directed to the equatorial plate
        4.    Anaphase II:  sister chromatids of each dyad are pulled to opposite poles (Haploid)
        5.    Telophase II:  monads and cytokinesis. Each chromosome is a monad (unreplicated)

VII.    Significance of Meiosis:
    A.    Function of Sexual reproduction and Meiosis
        1)    Maintain chromosome number
        2)    Increase genetic variability in individuals
         Sexual Reproduction:  occurs through production of sex cells or gametes.
               Gametes fuse to form the zygote: a single cell from which a new individual develops.
               General Scheme:
            -    Haploid (n) vs. Diploid (2n)
                    Homologous chromosomes
            -    Asexual Reproduction:
                    Single individual produces a new individual identical to itself.  Mitosis
                    Parthenogenetic: female organism can also produce offspring without fertilization.
    B.    Alternation of Generations in fungi and plants.